Dr.Pasupula Bhavani
Dr.Modini Pandharpurkar
Abstract
PURPOSE : TO REPORT A CASE OF CRANIOSYNOSTOSIS ANS ITS OCULAR OUTCOMES
METHODS : A 6 YEAR OLD CHILD PRESENTED TO THE OPD WITH CHIEF COMPLAINTS OF (RE) SEVERE PROTRUSION SINCE 1 MONTH ASSOCIATED WITH LOSS OF VISION. HISTORY OF FORWARD PROTRUSION OF BOTH EYES SINCE BIRTH WAS NOTED.FAMILY HISTORY AND MEDICAL HISTORY WAS INSIGNIFICANT .ABNORMAL FACIES OF HIS FATHER WAS NOTED WITH NORMAL VISION.
HISTORY OF SIMILAR COMPLAINTS TO THE (LE) 2 YEARS BACK FOR WHICH LE ENUCLEATION WAS DONE. ON EXAMINATION THE PATIENT HAS A WIDE NASAL BRIDGE,HYPERTELORISM AND EXOPHTHALMOS, INTRA ORAL EXAMINATION REVEALED HIGH ARCHED PALATE. CSF ANALYSIS- HIGH PRESSURES.CT SHOWING INCREASED AP DIAMETER OF SKULL WITH MULTIPLE AREAS OF OUTPOUCHING IN B/L FRONTAL SKULL VAULT WITH HERNIATION OF NEURAL ELEMENTS.
WITH THE ABOVE FINDINGS DIAGNOSIS OF CRANIOSYNOSTOSIS WAS MADE
RESULTS : PATIENT WAS TAKEN FOR RE ENUCLEATION AFTER NEUROSURGEON OPINION REGARDING THE OPTIC NERVE STATUS AND PROCEEDED WITH THE SURGERY .
